Double chambered right ventricle in adulthood: A case report and review of the literature

Background: The double chambered right ventricle (DCRV) is a rare congenital malformation, in which a dislocated hypertrophic muscular band causes the subdivision of the right ventricle in two chambers, proximal or high-pressure chamber and distal or low-pressure chamber. It is recommended to use echocardiography and cardiac catheterization for diagnosis. This case report seeks to provide additional data for comparison with existing literature, thereby contributing to a more comprehensive understanding of this condition. Case presentation: We are reporting the case of DCRV in an adult female, who was evaluated for shortness of breath. Diagnosis was confirmed by transthoracic echocardiography, with a maximal gradient of 97mmHg. The patient underwent a successful surgery. Conclusions: Most cases of classic DCRV are diagnosed in infant, and are associated with ventricular septal defect (VSD). Surgery is the most effective treatment by removing the muscular band.