Aneurysm and subacute type A aortic dissection, in a pediatric patient with aortopathy

Background aortic dissection in pediatrics is an extremely rare condition, which is generally related to predisposing factors such as connective tissue disorders, congenital heart disease and systemic arterial hypertension. Materials and methods: We report this case following the guidelines of the CARE guidelines. Results: A 3-year-old girl, with a history of bileaflet aortic valve (BAV), hypoplasia of the aortic arch and repaired aortic coarctation at one month of age. She was admitted 2 months of atypical chest pain, dysphonia, and low tone of voice. The echocardiogram and CT angiography showed an image corresponding to a Stanford A aortic dissection, with false lumen perfusion that generated a pseudoaneurysmal dilation with a saccular morphology of 53x40x70 mm dimensions. Exposure of the ascending aorta, aneurysmal dissection, and replacement with a 22 mm supracoronary tube were performed. The aortic arch branches were managed with the island technique after the proximal and distal anastomoses, with good postoperative evolution. Conclusion: We present a case of a 3-year-old pediatric patient with Stanford A aortic dissection, subacute evolution, with successful repair.